IDUA Antibody

Catalog Number:

47644

Amount:

100μg

Price:

$319

Swiss-Prot No:

Swiss-Prot#:P35475
NCBI Gene ID:3425
Gene Accssion:NP_000194

Form of Antibody:

Rabbit IgG in pH7.4 PBS, 0.05% NaN3, 40% Glycerol.

Storage/Stability:

Immunogen:

Synthetic peptide of human IDUA

Purification:

Antigen affinity purification

Specificity/Sensitivity:

The antibody detects endogenous levels of total IDUA protein.

Applications:

IHC

Background:

This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).?

References:

appl_detail:

IHC dilution:1: 30-150

Datasheet PDF