MCCC1 Antibody

Catalog Number:

47317

Amount:

100μg

Price:

$319

Swiss-Prot No:

Swiss-Prot#:Q96RQ3
NCBI Gene ID:56922
Gene Accssion:BC004187

Form of Antibody:

Rabbit IgG in pH7.4 PBS, 0.05% NaN3, 40% Glycerol.

Storage/Stability:

Immunogen:

Fusion protein of human MCCC1

Purification:

Antigen affinity purification

Specificity/Sensitivity:

The antibody detects endogenous levels of total MCCC1 protein.

Applications:

WB, IHC

Background:

This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

References:

appl_detail:

WB dilution:1:500-2000
IHC dilution:1: 40-200

Datasheet PDF