CLN5 Antibody

Catalog Number:

46515

Amount:

100μg

Price:

$319

Swiss-Prot No:

Swiss-Prot:O75503
NCBI Gene ID:1203
NCBI Protein:NP_006484

Form of Antibody:

Rabbit IgG in pH7.4 PBS, 0.05% NaN3, 40% Glycerol.

Storage/Stability:

Immunogen:

Synthetic peptide corresponding to internal residues of human CLN5

Purification:

Antigen affinity purification

Specificity/Sensitivity:

The antibody detects endogenous levels of total CLN5 protein.

Applications:

WB IHC

Background:

This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.

References:

appl_detail:

Western blotting: 1:200-1:1000
Immunohistochemistry: 1: 40-200

Datasheet PDF