Product Datasheet  
delta Sarcoglycan Antibody  
Catalog Number: 49501  
Technical:tech@swbio.com  
Information:info@swbio.com  
Description  
  • host_species:  
  • Rabbit
  • Amount:  
  • 100μgμg
  • Swiss-Prot No.:  
  • Swiss-Prot#:Q92629
  • Form of Antibody:  
  • 1*TBS (pH7.4), 1%BSA, 40%Glycerol. Preservative: 0.05% Sodium Azide.
  • Storage:  
  • Store at -20˚C
  • Immunogen:  
  • recombinant protein
  • reactivity:  
  • Hu
  • appl_detail:  
  • WB: 1:500-1:2,000
    IHC: 1:50-1:200

    IP: 1:10-1:50
  • other_names:  
  • 35 kDa dystrophin associated glycoprotein antibody
    35 kDa dystrophin-associated glycoprotein antibody
    35DAG antibody
    CMD1L antibody
    DAGD antibody
    Delta-sarcoglycan antibody
    Delta-SG antibody
    Dystrophin asso
  • Purification:  
  • ProA affinity purified
  • Specificity:  
  • Applications:  
  • WB, IP, IHC
  • Background:  
  • Component of the sarcoglycan complex, a subcomplex of the dystrophin-glycoprotein complex which forms a link between the F-actin cytoskeleton and the extracellular matrix. Defects in SGCD are the cause of limb-girdle muscular dystrophy type 2F (LGMD2F) [MIM:601287]. LGMD2F is an autosomal recessive disorder. Defects in SGCD are the cause of cardiomyopathy dilated type 1L (CMD1L) [MIM:606685]. Dilated cardiomyopathy is a disorder characterized by ventricular dilation and impaired systolic function, resulting in congestive heart failure and arrhythmia. Patients are at risk of premature death.



 
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